WORLD JOURNAL OF ADVANCE
HEALTHCARE RESEARCH

Akhil Mehrotra*, Mohammad Shaban and Faiz Illahi Siddiqui

ABSTRACT

Congenitally corrected transposition of the great arteries (CCTGA) is a rare congenital cardiac anomaly defined by atrio-ventricular and ventriculo-arterial discordance. This malformation makes up less than 1% of congenital heart defects. The hallmark of corrected transposition is discordance at atrio-ventricular and ventriculo-arterial level and that is defined as "double discordance". This can occur as an isolated anomaly but more commonly has associated defects; most common being ventricular septal defect followed by tricuspid valve abnormalities. Other associated defects are dextrocardia, pulmonary stenosis, systemic and pulmonary venous anomalies, univentricular physiology, ventricular dysfunction (morphological right ventricle facing systemic circulation) and association of conduction abnormalities. Echocardiography plays a pivotal role in defining the anatomy and planning the management. Situs Inversus is a rare congenital anomaly caused by the displacement of the organs in the chest and abdomen. Situs inversus totalis known as the displacement of all organs according to the mirror image. People having situs inversus totalis and dextrocardia live with normal life expectancy and are mostly asymptomatic. These anomalies may not be recognized for a long lifetime. Although, situs inversus totalis with dextrocardia are rare, the lack of a comprehensive study of this anomaly in the literature indicates that further research is needed. We report a case of a 29-year-old male who presented to our hospital with dyspnea on effort [New York Heart Association (NYHA) Functional Classification class II]. Subsequent echocardiographic study disclosed dextrocardia, situs inversus, CCTGA, pulmonary valvular stenosis with left sided aortic arch. This case highlights the association between such rare cardiac conditions.