WORLD JOURNAL OF ADVANCE
HEALTHCARE RESEARCH

Akhil Mehrotra*, Faiz Illahi Siddiqui, Mohammad Shaban, Ujala Shakya, Atul Mehrotra

ABSTRACT

Tricuspid atresia (TA) is a complex congenital heart disease that presents with cyanosis in the neonatal period. TAis associated with high mortality without early intervention. TA arises from either the agenesis (absence of rightatrioventricular connection) or the imperforation of the tricuspid valve. Consequently, there is no directcommunication between the right atrium and the right ventricle. Survival in patients with TA has been shown tobe hemodynamically dependent upon the presence of adequate pulmonary blood flow (PBF), a lack of elevatedpulmonary vascular resistance, and the degree of ventricular shunting. PBF is the most integral component ofthese factors. We are presenting a remarkable case of a seventeen year old female adolescent afflicted with TAalongwith severe central cyanosis, conspicuous clubbing in fingers of all the four extremities, atrial septal defect(ASD), ventricular septal defect (VSD), normally related great arteries (NRGA), hypoplastic right ventricle (RV)and dilated left ventricle (LV). It is noteworthy, that despite the protracted course of the illness, the patient has notundergone any palliative or surgical interventions till date.

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